Polysplenia Syndrome: A Rare Condition Discovered Incidentally
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Abstract
The Polysplenia Syndrome associates, in addition to the presence of several spleens, abnormalities falling within the framework of heterotaxy (situs inverses, pre-duodenal portal vein, absence of retro-hepatic IVC, Abnormal Hepatic Vascularization and intestinal malrotation). Case of a 32-year-old asthmatic patient who seeks therapy for abdominal pain and diarrhoea. Upon examination, it was discovered that the right iliac fossa and hypogastrium of the afebrile patient were tender. Acute appendicitis was thought to be the cause. The range of aberrant rotation of the thoraco-abdominal organs in Polysplenia Syndrome, a rare congenital disorder, differs from patient to patient. This syndrome's origin has not yet been determined.
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